Epidemiology of Dural Arteriovenous Fistulas in Children

Incidence and Prevalence

  • Rare: DAVF in children are rare. They represent up to 10% of all intracranial AV shunts in children. Only about 60 cases have been described in the literature(1).

Age Distribution

  • None: There is no age predilection.

Sex Predilection

  • None: There is no sex predilection.

Geographic distribution

  • None: There is no geographic distribution.

Risk Factors

  • Hypercoagulable states and sinus thrombosis: These should be systematically ruled out.
  • Previous surgery: In very rare occasions, surgical trauma to the meninges can induce the formation of DAVFs.
  • Previous trauma: In very rare occasions, head trauma can induce the formation of DAVFs.

Relationships to Other Disease States and Syndromes

  • DAVFs associated with genetically confirmed vascular anomaly syndromes: Walcott et al reported the association of two cases of dAVMs with PHACE and PTEN or Bannayan-Riley-Ruvalcaba syndromes(31).